Coexisting primary hyperparathyroidism and Albright's hereditary osteodystrophy--an unusual association.
نویسندگان
چکیده
Primary hyperparathyroidism associated with Albright's hereditary osteodystrophy was diagnosed in a 22 year old Japanese woman, the second such case to be reported. Albright's hereditary osteodystrophy (AHO) appears to be associated with a larger number of disorders than the well recognized pseudohypoparathyroidism. AHO and pseudo-pseudohypoparathyroidism are essentially identical.
منابع مشابه
Normocalcaemic pseudohypoparathyroidism with unusual phenotype.
We describe a boy who presented at 4 years of age with radiological hyperparathyroidism, osteosclerosis, and necrosis of the femoral heads. Plasma biochemistry was normal but the parathyroid hormone (PTH) level was very high. He was deaf and had an unusual facies but did not have the phenotype of Albright's hereditary osteodystrophy. Plasma and urine cyclic AMP reponses to bovine PTH were marke...
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ورودعنوان ژورنال:
- Postgraduate medical journal
دوره 61 712 شماره
صفحات -
تاریخ انتشار 1985